June 2008 - No- 9

Editor -Dr Rachel Evans

rachel.evans@swansea.tr.wales.nhs.uk
Editor's note

Welcome to our 9th Newsletter, only a month later than planned. 6 monthly newsletters have been introduced in a number of CF clinics throughout Europe, so it's nice to know that we are doing same as everyone else. As  per usual we are lacking contributions from you, all contributions to this new letter have come from the CF team.

Physiotherapists

Hi. It's me Julie today Michele is having a break after our trip to Prague for the ECFC (European CF Conference). More on that later. I know Michele has written before about the importance of exercise but I thought I would get your brain cells working this time. I'd like you to let me know what exercise you do! I don't mean formal school exercise, sport or arranged classes but what do you do that's fun or unusual. My children go to the beach and dig, run Lll and out of the sea or skateboard along the front. Or it could be dancing, kung fu, anything. Let me know on Julie.clarke@swansea-tr.wales.nhs.uk- you could even send me a photo. I'll look at them and put the most interesting- in the next newsletter.

The big news for physio from Prague is that Michele will be getting a cleaner for your e-flow membranes to keep them working as speedily as ever.

That's all from me I'm looking forward to hearing from you. Julie

Dorinda Holiday Time

When lucky to be going abroad on hols a letter from the CF team is not always required. On the other hand if travelling to America it is advisable to have some documentation. Travel Insurance remains an expensive item especially when insuring your CF child. There are lots available it would be advisable to shop around. Have a great time.

Schools
If any parent wishes me to visit  your child's school with regards to teachers and staff being aware of CF please contact me. Visits to Llandough

If any of you teenagers would like to visit the Adult CF unit in Llandough prior to your transfer to adult care I would be happy to discuss and take you. We always have a meal on the way home and it's our treat.

Ann (dietitian) Salt and fluid intake

If you are travelling to anywhere hot this summer or if we're lucky enough to have some hot days here please make sure that your CF child has extra salt to compensate for what they loose in their sweat. CF patients have more salt in their sweat than non CF individuals. For the older child / teenager this can be in the form of salt tablets. For the younger children just add some extra salt to their food. Symptoms of not enough salt in the blood (hyponatraemia) include' anorexia and vomiting. Also ensure they drink plenty of fluids.

Ciprofloxacin

If you child's prescribed ciprofloxacin during the summer months please remember that it makes their skin more photosensitive (i.e. they'll burn easier in the sun), so please be careful.

Trust Merger

Since April 1 st 2008 Swansea NHS Trust has merged with Bro Morgannwg NHS Trust to form Abertawe Bro MorgaIlLiwg (ABM) University NHS Trust. You might have noticed the new trust logo on the top of this news letter and on top of clinic letters.
This merger will not change any aspect of care of CF .child

 

European CF Conference

As a team we have just returned from the 31 st European CF conference in Prague. Lot of research ongoing in basic sciences looking at drugs directed at specific gene mutations which would lead to these cells producing some functioning CFTR (the chloride channel that is defective in CF). Ongoing work on drugs that might improve the salt (sodium and chloride) content of airway surface liquid so that secretions can be cleared easier from the lungs.
Different preparations of antibiotics for nebulisation or delivery by dry powder inhalers also under trial. Heard nothing on what's happening in gene therapy. Most research in past has been directed towards the lungs but there's an increasing interest in what's happening in the gastrointestinal tract of CF patients.

You can be reassured to learn that we seem to be doing the same as everyone else with regards to managing our CF patients at present. Our aim like other clinics is to keep our CF patients as well as possible with current management so that they would be able to benefit from any new developments in the future.

Fund raising

Many of you continue to raise money for our clinic and for the CF Trust by a variety of ways. Money donated to our clinic fund is used to buy equipment for children with CF or other long term respiratory
illness
and to help support the ongoing education of staff to ensure that we deliver best quality care. We and the CF Trust are very grateful to you all. We would like to mention the recent efforts of two people:

Jean Thomas one of our grandmothers who wrote a book "A Pictorial History of Penllegaer" and gave the clinic 50% of the profits; and one of our fathers Mark Thomas who ran the London Marathon and raised £2000 for the CF Trust. Please let us know about your fundraising efforts and we'll include them in our next newsletter. We'll be happy to advertise any fundraising event by putting a poster / flyer on the CF board in clinic.

Transition Clinic

We have been doing joint transition clinics with the adult CF team from Llandough since April 2005. Up till recently because of the back log of patients we needed to transfer we were only seeing the CF teenager once in the joint clinic before transferring their care to Llandough. Now that we are to up to date we would like to gradually introduce our CF teenagers to the adult team by seeing them in the joint transition clinic a few times in the years leading up to their transfer of care to Llandough. Our usual. age of transfer is between the ages of 16 and 18, exact age varies -between patients and depend on  patient wishes, schooling etc. We therefore will start offering appointments to the joint clinic from around the age of 14.

After School Clinic

We have been thinking of doing an after school clinic for our older patients (i.e. those in comprehensive school) for a number of years but haven't started because of a number of reasons including most of our children saying they prefelTed to 'come to clinic during school time. We would like to revisit this and will be asking you for your views over the next few months. Such a clinic would start late afternoon at around 3.30.

E-mail addresses

We had a disappointing response to our request for e-mail addresses in the last newsletter. We understand that you all, might not have an e-mail address but for those that do please let us have your e­ mail address so that we can communicate with you more efficiently. You can either e-mail Rachel (e-mail on top of newsletter) or let us know your e-mail address when you next come to clinic.

Next newletter

Next newsletter due November/ December 2008. Please send content suggestions or contributions to Rachel.